Primary perivascular epithelioid cell tumor of the liver: new case report and literature review

نویسندگان

  • Hassania Ameurtesse
  • Laïla Chbani
  • Amal Bennani
  • Imane Toughrai
  • Nouhad Beggui
  • Imane Kamaoui
  • Hinde Elfatemi
  • Taoufik Harmouch
  • Afaf Amarti
چکیده

UNLABELLED Perivascular epithelioid cell tumors (PEComas) encompass a group of rare mesenchymal neoplasms, which typically have a perivascular location with dual melanocytic and muscular differentiation. They are found in a variety of localizations, though lesions in the liver are exceedingly rare. Because of their rarity, the clinical, radiological and histological features of these tumors have yet to be established. This is why, it seems appropriate to report the observation of this rare hepatic tumor with a literary review including others published cases, assessing through it, clinicopathologic and radiologic features of all reported cases as well as their follow-up whenever possible. VIRTUAL SLIDES The virtual slide(s) for this article can be found here: http://www.diagnosticpathology.diagnomx.eu/vs/1967094999126169.

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عنوان ژورنال:

دوره 9  شماره 

صفحات  -

تاریخ انتشار 2014